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国际罕见病日 罕见病信息分析报告 1858-2022年

已有 1883 次阅读 2022-2-28 13:51 |个人分类:医学科普|系统分类:观点评述




        国际罕见病日,由欧洲罕见病组织(EURODIS)于2008年2月29日发起并组织了第一届国际罕见病日。首届国际罕见病日纪念活动在欧洲各国成功举行,通过各种活动促进了社会对罕见病的认识。2009年2月28日,欧洲北美拉丁美洲等30多个国家的罕见病组织参加了第二个国际罕见病日的活动,其后在各国的一致拥护下,将每年二月的最后一天定为国际罕见病日。

https://baike.baidu.com/item/%E5%9B%BD%E9%99%85%E7%BD%95%E8%A7%81%E7%97%85%E6%97%A5/9239245?fr=aladdin

关注罕见病 让爱不罕见2022-02-28 10:42

2月28日,国际罕见病日。全球已知的罕见病有7000多种。我国有2000多万罕见病患者,每年新增患者超20万。确诊难、治疗方法少、可用药品少等难题交织,让这个日益庞大的群体身陷困境。121种罕见病被纳入第一批罕见病目录、60余种罕见病用药获批上市、40余种罕见病用药被纳入国家医保药品目录……近年来,我国推进罕见病群体的医疗保障工作从未歇步。


罕见病信息分析报告

http://www.pubmedplus.cn/P/SearchQuickResult?wd=76476aeb-7f49-4262-9f23-2461f6a39f19


01.无法确认5465 篇1.757%
02.20222880 篇0.926%
03.202124416 篇7.852%
04.202021143 篇6.799%
05.201918290 篇5.882%
06.201816098 篇5.177%
07.201715656 篇5.035%
08.201615382 篇4.947%
09.201514642 篇4.709%
10.201414051 篇4.519%
11.201312709 篇4.087%
12.201211895 篇3.825%
13.201110715 篇3.446%
14.20109898 篇3.183%
15.20098980 篇2.888%
16.20088863 篇2.850%
17.20078157 篇2.623%
18.20067773 篇2.500%
19.20056839 篇2.199%
20.20046284 篇2.021%
21.20035942 篇1.911%
22.20025304 篇1.706%
23.20014760 篇1.531%
24.20004595 篇1.478%
25.19994110 篇1.322%
26.19984069 篇1.309%
27.19973730 篇1.200%
28.19963446 篇1.108%
29.19953240 篇1.042%
30.19942947 篇0.948%
31.19932803 篇0.901%
32.19922593 篇0.834%
33.19912342 篇0.753%
34.19902391 篇0.769%
35.19892271 篇0.730%
36.19881575 篇0.506%
37.19871505 篇0.484%
38.19861400 篇0.450%
39.19851401 篇0.451%
40.19841246 篇0.401%
41.19831131 篇0.364%
42.1982819 篇0.263%
43.1981870 篇0.280%
44.1980848 篇0.273%
45.1979804 篇0.259%
46.1978738 篇0.237%
47.1977721 篇0.232%
48.1976728 篇0.234%
49.1975597 篇0.192%
50.1974103 篇0.033%
51.197389 篇0.029%
52.197282 篇0.026%
53.197185 篇0.027%
54.197069 篇0.022%
55.196975 篇0.024%
56.196873 篇0.023%
57.196778 篇0.025%
58.196659 篇0.019%
59.1965127 篇0.041%
60.1964164 篇0.053%
61.1963120 篇0.039%
62.196296 篇0.031%
63.196182 篇0.026%
64.196091 篇0.029%
65.195972 篇0.023%
66.195876 篇0.024%
67.195775 篇0.024%
68.195678 篇0.025%
69.195581 篇0.026%
70.1954102 篇0.033%
71.195386 篇0.028%
72.195278 篇0.025%
73.195145 篇0.014%
74.195033 篇0.011%
75.194932 篇0.010%
76.194816 篇0.005%
77.194727 篇0.009%
78.194624 篇0.008%
79.19454 篇0.001%
80.19322 篇0.001%
81.19282 篇0.001%
82.19172 篇0.001%
83.19162 篇0.001%
84.19101 篇0.000%
85.19091 篇0.000%
86.18981 篇0.000%
87.18961 篇0.000%
88.18891 篇0.000%
89.18882 篇0.001%
90.18873 篇0.001%
91.18867 篇0.002%
92.18851 篇0.000%
93.18841 篇0.000%
94.18821 篇0.000%
95.18791 篇0.000%
96.18781 篇0.000%
97.18731 篇0.000%
98.18671 篇0.000%
99.18642 篇0.001%
100.18581 篇0.000%
01.bmj case rep3555 篇1.143%
02.orphanet j rare dis2785 篇0.896%
03.medicine (baltimore)2230 篇0.717%
04.cureus2019 篇0.649%
05.plos one1783 篇0.573%
06.j med case rep1275 篇0.410%
07.int j surg case rep1144 篇0.368%
08.ann thorac surg1044 篇0.336%
09.intern med1034 篇0.333%
10.j pediatr surg998 篇0.321%
01.美国69022 篇22.196%
02.中国23308 篇7.495%
03.意大利20779 篇6.682%
04.英国20032 篇6.442%
05.日本19659 篇6.322%
06.法国18005 篇5.790%
07.德国17510 篇5.631%
08.印度11589 篇3.727%
09.西班牙10011 篇3.219%
10.土耳其9769 篇3.142%
01.中国北京4815 篇1.548%
02.中国上海2652 篇0.853%
03.中国广州1391 篇0.447%
04.中国杭州1272 篇0.409%
05.中国成都1161 篇0.373%
06.中国香港1048 篇0.337%
07.中国南京836 篇0.269%
08.中国长沙805 篇0.259%
09.中国武汉752 篇0.242%
10.中国济南643 篇0.207%
01.Humans251551 篇80.895%
02.Female136304 篇43.833%
03.Male134679 篇43.311%
04.Adult85526 篇27.504%
05.Middle Aged79658 篇25.617%
06.Aged52188 篇16.783%
07.Adolescent32608 篇10.486%
08.Child32534 篇10.462%
09.Diagnosis, Differential27022 篇8.690%
10.Treatment Outcome26982 篇8.677%




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